Recent Advances in Systemic Scleroderma in Childhood
نویسندگان
چکیده
منابع مشابه
Recent Advances in Systemic Scleroderma in Childhood
Introduction Systemic sclerosis (SSc; scleroderma) is a systemic autoimmune disease characterised by diverse skin and internal organ involvement. The underlying pathology consists of fibrosis caused by fibroblast dysfunction and small vessel vasculopathy. It is much rarer in childhood, occurring only 1 in 1 million children, and comprises approximately 3-10% of the adult incidence [1,2]. Only o...
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©2014 Turkish League Against Rheumatism. All rights reserved. Juvenile systemic scleroderma is a rare chronic multi-system connective tissue disease in childhood. Although rare in children, it is an important cause of morbidity and mortality. Juvenile systemic scleroderma is one of the most severe rheumatologic conditions diagnosed in children. In this article, we report a six-year-old boy diag...
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Although many underlying diseases have been reported in the setting of childhood arterial ischemic stroke, emerging research demonstrates that non-atherosclerotic intracerebral arteriopathies in otherwise healthy children are prevalent. Minor infections may play a role in arteriopathies that have no other apparent underlying cause. Although stroke in childhood differs in many aspects from adult...
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ژورنال
عنوان ژورنال: Annals of Paediatric Rheumatology
سال: 2014
ISSN: 2146-2909
DOI: 10.5455/apr.120420141451